Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001389959 | SCV001591520 | pathogenic | not provided | 2020-11-19 | criteria provided, single submitter | clinical testing | For these reasons, this variant has been classified as Pathogenic. This variant has been observed in individual(s) with retinitis pigmentosa (PMID: 21069908). This variant is not present in population databases (ExAC no frequency). This sequence change creates a premature translational stop signal (p.Gln27Argfs*16) in the EYS gene. It is expected to result in an absent or disrupted protein product. Loss-of-function variants in EYS are known to be pathogenic (PMID: 18836446, 20333770). |
Baylor Genetics | RCV003469562 | SCV004193542 | likely pathogenic | Retinitis pigmentosa 25 | 2023-01-19 | criteria provided, single submitter | clinical testing | |
Fulgent Genetics, |
RCV003469562 | SCV005672771 | pathogenic | Retinitis pigmentosa 25 | 2024-06-13 | criteria provided, single submitter | clinical testing |