Total submissions: 5
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV001723462 | SCV003837012 | uncertain significance | not provided | 2022-08-30 | criteria provided, single submitter | clinical testing | Nonsense variant predicted to result in protein truncation or nonsense mediated decay in a gene for which loss of function is a known mechanism of disease; Has not been previously published as pathogenic or benign to our knowledge |
Juno Genomics, |
RCV004796652 | SCV005416834 | likely pathogenic | Autosomal recessive nonsyndromic hearing loss 84A | criteria provided, single submitter | clinical testing | PM2_Supporting+PVS1 | |
Institute of Rare Diseases, |
RCV004796652 | SCV005687307 | pathogenic | Autosomal recessive nonsyndromic hearing loss 84A | 2025-01-09 | criteria provided, single submitter | research | PVS1;PM3_Supporting;PM2_Supporting |
Joint Genome Diagnostic Labs from Nijmegen and Maastricht, |
RCV001723462 | SCV001958710 | pathogenic | not provided | no assertion criteria provided | clinical testing | ||
Clinical Genetics DNA and cytogenetics Diagnostics Lab, |
RCV001723462 | SCV001975030 | pathogenic | not provided | no assertion criteria provided | clinical testing |