Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV004721578 | SCV005327833 | likely pathogenic | not provided | 2023-11-17 | criteria provided, single submitter | clinical testing | In silico analysis supports that this missense variant has a deleterious effect on protein structure/function; Not observed at significant frequency in large population cohorts (gnomAD); This variant is associated with the following publications: (PMID: 30872814) |
Center for Statistical Genetics, |
RCV000754559 | SCV000853297 | uncertain significance | Hearing impairment | 2018-10-08 | no assertion criteria provided | research | |
OMIM | RCV001003504 | SCV001162357 | pathogenic | Hearing loss, autosomal dominant 76 | 2020-02-21 | no assertion criteria provided | literature only | |
University of Washington Center for Mendelian Genomics, |
RCV001261780 | SCV001439103 | uncertain significance | Autosomal dominant nonsyndromic hearing impairment | no assertion criteria provided | research |