Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
New York Genome Center | RCV001839204 | SCV002099152 | uncertain significance | SIN3A-related intellectual disability syndrome due to a point mutation | 2021-04-16 | criteria provided, single submitter | clinical testing | The inherited heterozygous c.3346C>T (p.Arg1116Cys) variant identified in the SIN3A gene has not been reported in affected individuals in the literature. The variant is absent from gnomAD(v3) database suggestingit is not a common benign variant in the populations represented in that database. The variant affects an evolutionarily conserved residue and is predicted deleterious by multiple in silico prediction tools. Given the lack of compelling evidence for its pathogenicity, the inherited heterozygous c.3346C>T (p.Arg1116Cys) variant identified in the SIN3A gene is reported as a variant of uncertain significance. |