Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Laboratory for Molecular Medicine, |
RCV000037056 | SCV000060712 | likely benign | not specified | 2013-01-25 | criteria provided, single submitter | clinical testing | Phe270Phe in exon 7 of MYH14: This variant is not expected to have clinical sign ificance because it does not alter an amino acid residue, it is not located with in the conserved splice consensus sequence, and it has been identified in 0.01% (1/8600) of European American chromosomes from a broad population by the NHLBI E xome Sequencing Project (http://evs.gs.washington.edu/EVS/). |
Gene |
RCV000037056 | SCV000720715 | likely benign | not specified | 2017-07-07 | criteria provided, single submitter | clinical testing | This variant is considered likely benign or benign based on one or more of the following criteria: it is a conservative change, it occurs at a poorly conserved position in the protein, it is predicted to be benign by multiple in silico algorithms, and/or has population frequency not consistent with disease. |
Ce |
RCV003407406 | SCV004140502 | likely benign | not provided | 2022-09-01 | criteria provided, single submitter | clinical testing | MYH14: BP4, BP7 |
Labcorp Genetics |
RCV003407406 | SCV004548059 | uncertain significance | not provided | 2023-05-09 | criteria provided, single submitter | clinical testing | This sequence change affects codon 262 of the MYH14 mRNA. It is a 'silent' change, meaning that it does not change the encoded amino acid sequence of the MYH14 protein. It affects a nucleotide within the consensus splice site. This variant is present in population databases (rs374146214, gnomAD 0.04%), and has an allele count higher than expected for a pathogenic variant. This variant has not been reported in the literature in individuals affected with MYH14-related conditions. ClinVar contains an entry for this variant (Variation ID: 44080). Algorithms developed to predict the effect of sequence changes on RNA splicing suggest that this variant is not likely to affect RNA splicing. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |