Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Baylor Genetics | RCV001328620 | SCV001519777 | uncertain significance | Cardiac arrhythmia, ankyrin-B-related | 2019-10-10 | criteria provided, single submitter | clinical testing | This variant was determined to be of uncertain significance according to ACMG Guidelines, 2015 [PMID:25741868]. |
Ambry Genetics | RCV002395731 | SCV002700254 | uncertain significance | Cardiovascular phenotype | 2020-06-30 | criteria provided, single submitter | clinical testing | The p.P3459A variant (also known as c.10375C>G), located in coding exon 38 of the ANK2 gene, results from a C to G substitution at nucleotide position 10375. This exon is expressed solely in brain (Mohler PJ et al. Circulation. 2007;115(4):432-41). The proline at codon 3459 is replaced by alanine, an amino acid with highly similar properties. This amino acid position is well conserved in available vertebrate species. In addition, the in silico prediction for this alteration is inconclusive. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |
Fulgent Genetics, |
RCV001328620 | SCV002783281 | uncertain significance | Cardiac arrhythmia, ankyrin-B-related | 2021-09-13 | criteria provided, single submitter | clinical testing |