Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Mayo Clinic Laboratories, |
RCV000681637 | SCV000809083 | uncertain significance | Mitochondrial DNA depletion syndrome 12B (cardiomyopathic type), autosomal recessive | 2018-06-01 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV001868308 | SCV002276995 | uncertain significance | not provided | 2021-12-02 | criteria provided, single submitter | clinical testing | Algorithms developed to predict the effect of missense changes on protein structure and function are either unavailable or do not agree on the potential impact of this missense change (SIFT: "Deleterious"; PolyPhen-2: "Probably Damaging"; Align-GVGD: "Class C15"). ClinVar contains an entry for this variant (Variation ID: 562200). This variant has not been reported in the literature in individuals affected with SLC25A4-related conditions. This variant is not present in population databases (gnomAD no frequency). This sequence change replaces glycine, which is neutral and non-polar, with valine, which is neutral and non-polar, at codon 172 of the SLC25A4 protein (p.Gly172Val). In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |