Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Genomic Research Center, |
RCV000661929 | SCV000784254 | uncertain significance | X-linked myopathy with postural muscle atrophy | 2018-03-05 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV000661929 | SCV001565753 | uncertain significance | X-linked myopathy with postural muscle atrophy | 2020-01-23 | criteria provided, single submitter | clinical testing | In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. Algorithms developed to predict the effect of missense changes on protein structure and function are either unavailable or do not agree on the potential impact of this missense change (SIFT: "Tolerated"; PolyPhen-2: "Possibly Damaging"; Align-GVGD: "Class C0"). This variant has not been reported in the literature in individuals with FHL1-related conditions. ClinVar contains an entry for this variant (Variation ID: 548468). This variant is not present in population databases (ExAC no frequency). This sequence change replaces valine with methionine at codon 151 of the FHL1 protein (p.Val151Met). The valine residue is moderately conserved and there is a small physicochemical difference between valine and methionine. |