Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Genomic Research Center, |
RCV000662006 | SCV000784338 | likely pathogenic | Desbuquois dysplasia 1 | 2018-03-05 | criteria provided, single submitter | clinical testing | |
Genomic Research Center, |
RCV000662007 | SCV000784339 | likely pathogenic | Epiphyseal dysplasia, multiple, 7 | 2018-03-05 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV001855396 | SCV002227122 | uncertain significance | not provided | 2021-09-02 | criteria provided, single submitter | clinical testing | This sequence change replaces alanine with valine at codon 371 of the CANT1 protein (p.Ala371Val). The alanine residue is highly conserved and there is a small physicochemical difference between alanine and valine. This variant is present in population databases (rs372631124, ExAC 0.05%). This variant has not been reported in the literature in individuals affected with CANT1-related conditions. ClinVar contains an entry for this variant (Variation ID: 548509). Algorithms developed to predict the effect of missense changes on protein structure and function are either unavailable or do not agree on the potential impact of this missense change (SIFT: "Deleterious"; PolyPhen-2: "Probably Damaging"; Align-GVGD: "Class C0"). In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |