Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001932262 | SCV002126098 | uncertain significance | Autosomal recessive limb-girdle muscular dystrophy type 2W | 2023-05-01 | criteria provided, single submitter | clinical testing | ClinVar contains an entry for this variant (Variation ID: 1362387). An algorithm developed to predict the effect of missense changes on protein structure and function (PolyPhen-2) suggests that this variant  is likely to be tolerated. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. This variant has not been reported in the literature in individuals affected with LIMS2-related conditions. This sequence change replaces serine, which is neutral and polar, with leucine, which is neutral and non-polar, at codon 29 of the LIMS2 protein (p.Ser29Leu). This variant is present in population databases (rs369093987, gnomAD 0.006%). |
Revvity Omics, |
RCV001932262 | SCV003814653 | uncertain significance | Autosomal recessive limb-girdle muscular dystrophy type 2W | 2022-04-15 | criteria provided, single submitter | clinical testing |