Total submissions: 5
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV000196846 | SCV000252291 | uncertain significance | not provided | 2014-10-28 | criteria provided, single submitter | clinical testing | p.Thr323Ile (ACC>ATC): c.968 C>T in exon 8 of the SLC37A4 gene (NM_001164277.1) A variant of unknown significance has been identified in the SLC37A4 gene. The T323I variant has not been published as a mutation, nor has it been reported as a benign polymorphism to our knowledge. Mutations in the SLC37A4 gene are associated with the autosomal recessive disorders glycogen storage disease Ib and Ic. The T323I variant is a non-conservative amino acid substitution, which is likely to impact secondary protein structure as these residues differ in polarity, charge, size and/or other properties. This substitution occurs at a position where amino acids similar to Threonine are conserved across species. In silico analysis is inconsistent in its predictions as to whether or not the variant is damaging to the protein structure/function. Therefore, based on the currently available information, it is unclear whether this variant is a pathogenic mutation or a rare benign variant. The variant is found in MITONUC-MITOP panel(s). |
Labcorp Genetics |
RCV001084427 | SCV001027625 | benign | Glucose-6-phosphate transport defect | 2024-01-30 | criteria provided, single submitter | clinical testing | |
Genome- |
RCV001084427 | SCV001652736 | likely benign | Glucose-6-phosphate transport defect | 2021-05-18 | criteria provided, single submitter | clinical testing | |
Ce |
RCV000196846 | SCV004129447 | benign | not provided | 2022-08-01 | criteria provided, single submitter | clinical testing | SLC37A4: BP4, BS1, BS2 |
Prevention |
RCV003937743 | SCV004756069 | benign | SLC37A4-related disorder | 2019-06-02 | no assertion criteria provided | clinical testing | This variant is classified as benign based on ACMG/AMP sequence variant interpretation guidelines (Richards et al. 2015 PMID: 25741868, with internal and published modifications). |