Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Rady Children's Institute for Genomic Medicine, |
RCV001267672 | SCV001445905 | pathogenic | Nemaline myopathy 2 | 2019-05-15 | criteria provided, single submitter | clinical testing | This variant affects the canonical splice donor site of intron 73 and is therefore predicted to interfere with splicing and result in loss of normal protein function. This variant has not been previously reported or functionally characterized in the literature to our knowledge. A different variant at the same position (c.10872+1G>T) has been reported in the homozygous state in a patient with fetal akinesia (PMID: 28336317). Multiple splice prediction tools suggest this variant is likely to interfere with normal splicing. Based on the available evidence, the c.10872+1G>A variant is classified as a Pathogenic. |