Total submissions: 7
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000546780 | SCV000640765 | benign | Nemaline myopathy 2 | 2024-01-30 | criteria provided, single submitter | clinical testing | |
Illumina Laboratory Services, |
RCV000546780 | SCV001293802 | uncertain significance | Nemaline myopathy 2 | 2017-04-27 | criteria provided, single submitter | clinical testing | This variant was observed as part of a predisposition screen in an ostensibly healthy population. A literature search was performed for the gene, cDNA change, and amino acid change (where applicable). No publications were found based on this search. Allele frequency data from public databases did not allow this variant to be ruled in or out of causing disease. Therefore, this variant is classified as a variant of unknown significance. |
Ambry Genetics | RCV002526138 | SCV003740047 | uncertain significance | Inborn genetic diseases | 2021-10-22 | criteria provided, single submitter | clinical testing | The c.2771A>C (p.Y924S) alteration is located in exon 28 (coding exon 26) of the NEB gene. This alteration results from a A to C substitution at nucleotide position 2771, causing the tyrosine (Y) at amino acid position 924 to be replaced by a serine (S). Based on insufficient or conflicting evidence, the clinical significance of this alteration remains unclear. |
Revvity Omics, |
RCV003133324 | SCV003811549 | uncertain significance | not provided | 2019-11-26 | criteria provided, single submitter | clinical testing | |
Ce |
RCV003133324 | SCV005075145 | uncertain significance | not provided | 2024-06-01 | criteria provided, single submitter | clinical testing | NEB: PM2, BP1 |
Gene |
RCV003133324 | SCV005327020 | uncertain significance | not provided | 2024-03-18 | criteria provided, single submitter | clinical testing | Identified in a patient with adult-onset myopathy along with NEB variant c.21790G>C. The phase of these two variants (cis/trans) is unknown (Poster presentation; Morales et al., 2017); Also reported in one patient in association with endometriosis; however, rurther research is needed to explore a possible link between variants in the NEB gene and this phenotype (PMID: 37626618); In silico analysis supports that this missense variant has a deleterious effect on protein structure/function; This variant is associated with the following publications: (PMID: 37626618) |
Natera, |
RCV000546780 | SCV002077774 | uncertain significance | Nemaline myopathy 2 | 2019-11-11 | no assertion criteria provided | clinical testing |