Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001958711 | SCV002240200 | pathogenic | Leber congenital amaurosis 12 | 2021-11-09 | criteria provided, single submitter | clinical testing | For these reasons, this variant has been classified as Pathogenic. This variant has not been reported in the literature in individuals affected with RD3-related conditions. This variant is present in population databases (rs761112550, gnomAD 0.0009%). This sequence change creates a premature translational stop signal (p.Ser5Metfs*18) in the RD3 gene. It is expected to result in an absent or disrupted protein product. Loss-of-function variants in RD3 are known to be pathogenic (PMID: 23308101). |
Gene |
RCV004591665 | SCV005079632 | likely pathogenic | not provided | 2024-01-07 | criteria provided, single submitter | clinical testing | Frameshift variant predicted to result in protein truncation or nonsense mediated decay in a gene for which loss of function is a known mechanism of disease; Not observed at significant frequency in large population cohorts (gnomAD); Has not been previously reported as pathogenic or benign in association with RD3-related disorders to our knowledge; This variant is associated with the following publications: (PMID: 31964843) |