Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Illumina Laboratory Services, |
RCV002260560 | SCV002540246 | uncertain significance | Generalized epilepsy with febrile seizures plus | 2021-12-21 | criteria provided, single submitter | clinical testing | The SCN1A c.2636T>C (p.Leu879Pro) missense variant results in the substitution of leucine at amino acid position 879 with proline. This variant has been reported in a heterozygous state in one individual with Dravet syndrome (Møller et al. 2016; Brunklaus et al. 2020; Johannesen et al. 2020). Inheritance information was unavailable for this patient. This variant is not found in version 2.1.1 or version 3.1.2 of the Genome Aggregation Database. The c.2636T>C variant is located in the D2 transmembrane domain and multiple lines of computational evidence suggest the variant may have a deleterious effect on the gene or gene product. Based on the available evidence, the c.2636T>C (p.Leu879Pro) variant is classified as a variant of uncertain significance for generalized epilepsy with febrile seizures plus. |