Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Athena Diagnostics | RCV000517765 | SCV000615028 | uncertain significance | not specified | 2016-12-29 | criteria provided, single submitter | clinical testing | |
Gene |
RCV001569815 | SCV001793970 | likely benign | not provided | 2020-04-30 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV002525077 | SCV003298877 | uncertain significance | Early infantile epileptic encephalopathy with suppression bursts | 2022-07-14 | criteria provided, single submitter | clinical testing | Variants that disrupt the consensus splice site are a relatively common cause of aberrant splicing (PMID: 17576681, 9536098). Algorithms developed to predict the effect of sequence changes on RNA splicing suggest that this variant is not likely to affect RNA splicing. This sequence change falls in intron 15 of the SCN1A gene. It does not directly change the encoded amino acid sequence of the SCN1A protein. It affects a nucleotide within the consensus splice site. This variant is present in population databases (no rsID available, gnomAD 0.0009%). This variant has not been reported in the literature in individuals affected with SCN1A-related conditions. ClinVar contains an entry for this variant (Variation ID: 448250). In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |