Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Fulgent Genetics, |
RCV002475996 | SCV002782748 | uncertain significance | Autosomal recessive inherited pseudoxanthoma elasticum; Pseudoxanthoma elasticum, forme fruste; Arterial calcification, generalized, of infancy, 2 | 2021-09-23 | criteria provided, single submitter | clinical testing | |
Ce |
RCV003456402 | SCV004184542 | uncertain significance | not provided | 2023-11-01 | criteria provided, single submitter | clinical testing | ABCC6: PP2, BP4 |
PXE International | RCV000499196 | SCV000589205 | uncertain significance | Autosomal recessive inherited pseudoxanthoma elasticum | 2021-02-04 | no assertion criteria provided | research | |
Prevention |
RCV004737571 | SCV005350645 | uncertain significance | ABCC6-related disorder | 2024-09-21 | no assertion criteria provided | clinical testing | The ABCC6 c.232G>A variant is predicted to result in the amino acid substitution p.Ala78Thr. This variant was previously reported in a large cohort of individuals with pseudoxanthoma elasticum, although no detailed clinical or genetic information was provided (Jin et al. 2015. PubMed ID: 25615550). This variant was also reported in an individual with Tetralogy of Fallot (Pan et al. 2022. PubMed ID: 36071769). This variant is reported in 0.53% of alleles in individuals of East Asian descent in gnomAD. This variant falls within a highly paralogous region. Allele frequency data should be interpreted with caution. At this time, the clinical significance of this variant is uncertain due to the absence of conclusive functional and genetic evidence. |