Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV000479505 | SCV000573313 | uncertain significance | not provided | 2017-02-20 | criteria provided, single submitter | clinical testing | A variant of uncertain significance has been identified in the PCDH19 gene. The c.570_572dupCGT variant has not been published as a pathogenic variant, nor has it been reported as a benign variant to our knowledge. The c.570_572dupCGT variant is not observed in large population cohorts (Lek et al., 2016; 1000 Genomes Consortium et al., 2015; Exome Variant Server). The c.570_572dupCGT variant results in an in-frame duplication of a single Valine residue, denoted p.V192dup. This duplication occurs at a position that is conserved across species. Therefore, based on the currently available information, it is unclear whether this variant is a pathogenic variant or a rare benign variant. |