Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Laboratory of Molecular Genetics |
RCV001374926 | SCV001572213 | likely pathogenic | Neurodevelopmental disorder | 2021-03-11 | criteria provided, single submitter | clinical testing | |
Laboratoire de Génétique Moléculaire, |
RCV003148986 | SCV003836716 | likely pathogenic | Wiedemann-Steiner syndrome | 2021-06-01 | criteria provided, single submitter | clinical testing | |
Gene |
RCV004770128 | SCV005377829 | likely pathogenic | not provided | 2024-04-15 | criteria provided, single submitter | clinical testing | Not observed at significant frequency in large population cohorts (gnomAD); In silico analysis supports that this missense variant has a deleterious effect on protein structure/function; In silico analysis also supports that this variant has a deleterious effect on splicing.; This variant is associated with the following publications: (PMID: 34828665) |