Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV002527015 | SCV003524839 | pathogenic | Primary pulmonary hypertension | 2022-04-28 | criteria provided, single submitter | clinical testing | This sequence change creates a premature translational stop signal (p.Gln450*) in the BMPR2 gene. It is expected to result in an absent or disrupted protein product. Loss-of-function variants in BMPR2 are known to be pathogenic (PMID: 16429395). This variant is not present in population databases (gnomAD no frequency). This premature translational stop signal has been observed in individual(s) with pulmonary arterial hypertension (PMID: 15591269). ClinVar contains an entry for this variant (Variation ID: 425927). For these reasons, this variant has been classified as Pathogenic. |
Rare Disease Genomics Group, |
RCV000488691 | SCV000576222 | pathogenic | Pulmonary hypertension, primary, 1 | no assertion criteria provided | literature only |