Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV004969990 | SCV005539219 | uncertain significance | Inborn genetic diseases | 2024-11-18 | criteria provided, single submitter | clinical testing | The p.I562V variant (also known as c.1684A>G), located in coding exon 12 of the BMPR2 gene, results from an A to G substitution at nucleotide position 1684. The isoleucine at codon 562 is replaced by valine, an amino acid with highly similar properties. This amino acid position is conserved. In addition, this alteration is predicted to be tolerated by in silico analysis. Based on the available evidence, the clinical significance of this variant remains unclear. |
Fulgent Genetics, |
RCV005023748 | SCV005654568 | uncertain significance | Pulmonary hypertension, primary, 1; Pulmonary venoocclusive disease 1 | 2024-01-21 | criteria provided, single submitter | clinical testing |