Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
OMIM | RCV003984810 | SCV000056380 | pathogenic | Pulmonary venoocclusive disease 1 | 2008-07-01 | no assertion criteria provided | literature only | |
UF D’onco_angiogenetique Et Genomique Des Tumeurs Solides, |
RCV003227622 | SCV003924093 | uncertain significance | Familial pulmonary capillary hemangiomatosis | 2023-05-12 | no assertion criteria provided | clinical testing | This variant was identified in a patient with PVOD (same patient as the one described in PMID: 18626305) for whom a biallelic pathogenic variant was identified in the EIF2AK4 gene (PMID: 24292273. |