Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Hacettepe Pediatric Genetics Laboratory, |
RCV004698890 | SCV004697973 | likely pathogenic | Boudin-Mortier syndrome | 2024-03-04 | criteria provided, single submitter | clinical testing | Homozygous c.691_692del (p.Thr231ValfsTer24) variant in NPR3 gene is classified as “likely pathogenic” according to the ACMG 2015 criteria (PVS1, PM2) and absent in gnomAD browser. |