Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000538535 | SCV000624020 | uncertain significance | Primary ciliary dyskinesia | 2022-07-03 | criteria provided, single submitter | clinical testing | This sequence change replaces arginine, which is basic and polar, with histidine, which is basic and polar, at codon 1737 of the DNAH8 protein (p.Arg1737His). This variant is present in population databases (rs568480936, gnomAD 0.05%). This variant has not been reported in the literature in individuals affected with DNAH8-related conditions. ClinVar contains an entry for this variant (Variation ID: 454578). Algorithms developed to predict the effect of missense changes on protein structure and function are either unavailable or do not agree on the potential impact of this missense change (SIFT: "Deleterious"; PolyPhen-2: "Not Available"; Align-GVGD: "Class C0"). In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |
Johns Hopkins Genomics, |
RCV002282202 | SCV002570343 | uncertain significance | Spermatogenic failure 46 | 2022-08-31 | criteria provided, single submitter | clinical testing | This DNAH8 missense variant (rs568480936) is rare (<0.1%) in a large population dataset (gnomAD v2.1.1: 21/250132 total alleles; 0.0084%; no homozygotes). It has been reported in ClinVar (Variation ID 454578), but has not been reported in the literature, to our knowledge. Two bioinformatic tools queried predict that this substitution would be damaging, and the arginine residue at this position is evolutionarily conserved across many of the species assessed. The contribution of DNAH8 to primary ciliary dyskinesia has not been confirmed. We consider the clinical significance of c.5210G>A in DNAH8 to be uncertain at this time. |
Ambry Genetics | RCV004023707 | SCV003941118 | uncertain significance | not specified | 2023-06-12 | criteria provided, single submitter | clinical testing | The c.5210G>A (p.R1737H) alteration is located in exon 38 (coding exon 37) of the DNAH8 gene. This alteration results from a G to A substitution at nucleotide position 5210, causing the arginine (R) at amino acid position 1737 to be replaced by a histidine (H). Based on insufficient or conflicting evidence, the clinical significance of this alteration remains unclear. |