Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001946380 | SCV002211540 | uncertain significance | Mosaic variegated aneuploidy syndrome 1 | 2021-12-11 | criteria provided, single submitter | clinical testing | This sequence change replaces tryptophan, which is neutral and slightly polar, with leucine, which is neutral and non-polar, at codon 978 of the BUB1B protein (p.Trp978Leu). In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. Algorithms developed to predict the effect of missense changes on protein structure and function (SIFT, PolyPhen-2, Align-GVGD) all suggest that this variant is likely to be tolerated. This variant has not been reported in the literature in individuals affected with BUB1B-related conditions. This variant is present in population databases (no rsID available, gnomAD 0.01%). |
Ambry Genetics | RCV004970579 | SCV005546107 | uncertain significance | Inborn genetic diseases | 2024-07-13 | criteria provided, single submitter | clinical testing | The p.W978L variant (also known as c.2933G>T), located in coding exon 22 of the BUB1B gene, results from a G to T substitution at nucleotide position 2933. The tryptophan at codon 978 is replaced by leucine, an amino acid with similar properties. This amino acid position is conserved. In addition, the in silico prediction for this alteration is inconclusive. Based on the available evidence, the clinical significance of this variant remains unclear. |