Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001037583 | SCV001201006 | uncertain significance | Cryopyrin associated periodic syndrome | 2022-09-14 | criteria provided, single submitter | clinical testing | In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. Algorithms developed to predict the effect of missense changes on protein structure and function output the following: SIFT: "Tolerated"; PolyPhen-2: "Benign"; Align-GVGD: "Class C0". The alanine amino acid residue is found in multiple mammalian species, which suggests that this missense change does not adversely affect protein function. ClinVar contains an entry for this variant (Variation ID: 836449). This variant has not been reported in the literature in individuals affected with NLRP3-related conditions. This variant is not present in population databases (gnomAD no frequency). This sequence change replaces serine, which is neutral and polar, with alanine, which is neutral and non-polar, at codon 387 of the NLRP3 protein (p.Ser387Ala). |
Fulgent Genetics, |
RCV002481858 | SCV002788072 | uncertain significance | Chronic infantile neurological, cutaneous and articular syndrome; Keratitis fugax hereditaria; Familial amyloid nephropathy with urticaria AND deafness; Familial cold autoinflammatory syndrome 1; Hearing loss, autosomal dominant 34, with or without inflammation | 2022-03-24 | criteria provided, single submitter | clinical testing | |
Institute for Clinical Genetics, |
RCV003321783 | SCV004026246 | uncertain significance | not provided | 2023-01-03 | criteria provided, single submitter | clinical testing |