Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Genome Diagnostics Laboratory, |
RCV001848477 | SCV002104825 | uncertain significance | Hereditary spastic paraplegia | 2018-02-01 | criteria provided, single submitter | clinical testing | |
Revvity Omics, |
RCV003130555 | SCV003814549 | uncertain significance | not provided | 2020-01-30 | criteria provided, single submitter | clinical testing | |
Neuberg Centre For Genomic Medicine, |
RCV003446926 | SCV004171949 | uncertain significance | Intellectual disability, autosomal dominant 9 | criteria provided, single submitter | clinical testing | The observed missense c.182C>T(p.Ser61Leu) variant in KIF1A gene has not been reported previously as a pathogenic variant nor as a benign variant, to our knowledge. The p.Ser61Leu variant is absent in gnomAD Exomes. This variant has been submitted to the ClinVar database as Uncertain significance. The amino acid change p.Ser61Leu in KIF1A is predicted as conserved by GERP++ and PhyloP across 100 vertebrates. The amino acid Ser at position 61 is changed to a Leu changing protein sequence and it might alter its composition and physico-chemical properties. For these reasons, this variant has been classified as Variant of Uncertain Significance (VUS). |