Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV002265063 | SCV002546691 | pathogenic | not provided | 2022-07-05 | criteria provided, single submitter | clinical testing | Not observed at significant frequency in large population cohorts (gnomAD); In silico analysis supports that this missense variant has a deleterious effect on protein structure/function; This variant is associated with the following publications: (PMID: 34140661) |
Institute of Human Genetics Munich, |
RCV002468655 | SCV002764978 | pathogenic | Microcytic anemia; 3-Methylglutaric aciduria; 3-Methylglutaconic aciduria; Myeloid maturation arrest | 2020-11-13 | criteria provided, single submitter | clinical testing | |
OMIM | RCV002221966 | SCV002499264 | pathogenic | 3-methylglutaconic aciduria, type VIIB | 2022-08-11 | no assertion criteria provided | literature only |