Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV000489754 | SCV000576868 | uncertain significance | not provided | 2017-04-17 | criteria provided, single submitter | clinical testing | The c.1693delT variant in the TTN gene has not been reported previously as a pathogenic variant nor as a benign variant, to our knowledge. The c.1693del variant causes a frameshift starting with codon Serine 565, changes this amino acid to a Proline residue, and creates a premature Stop codon at position 4 of the new reading frame, denoted p.Ser565ProfsX4. This variant is predicted to cause loss of normal protein function either through protein truncation or nonsense-mediated mRNA decay. However, the c.1693delT variant is located within the Z-disk region of TTN. The c.1693delT variant is not observed in large population cohorts (Lek et al., 2016; 1000 Genomes Consortium et al., 2015; Exome Variant Server). We interpret c.1693delT as a variant of uncertain significance. |
CHEO Genetics Diagnostic Laboratory, |
RCV000770159 | SCV000901585 | uncertain significance | Cardiomyopathy | 2017-07-31 | criteria provided, single submitter | clinical testing |