Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Laboratory for Molecular Medicine, |
RCV001195641 | SCV001366040 | uncertain significance | not specified | 2019-08-28 | criteria provided, single submitter | clinical testing | The p.Ala11147Thr variant in TTN has not been previously reported in individuals with cardiomyopathy, but has been identified in 0.001% (1/112304) of European chromosomes by gnomAD (http://gnomad.broadinstitute.org). Computational prediction tools and conservation analyses suggest that this variant may impact the protein, though this information is not predictive enough to determine pathogenicity. In summary, the clinical significance of this variant is uncertain. ACMG/AMP criteria applied: PM2, PP3. |