Total submissions: 5
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Biesecker Lab/Clinical Genomics Section, |
RCV000172341 | SCV000055004 | uncertain significance | not provided | 2013-06-24 | criteria provided, single submitter | research | |
Eurofins Ntd Llc |
RCV000172341 | SCV000334410 | uncertain significance | not provided | 2015-08-21 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV000617390 | SCV000737097 | uncertain significance | Cardiovascular phenotype | 2016-06-16 | criteria provided, single submitter | clinical testing | The p.R4743H variant (also known as c.14228G>A), located in coding exon 53 of the TTN gene, results from a G to A substitution at nucleotide position 14228. This alteration is located in the I-band region of the N2-B isoform of the titin protein. The arginine at codon 4743 is replaced by histidine, an amino acid with highly similar properties. This alteration has been reported as a secondary cardiac variant in an exome cohort (Ng D et al. Circ Cardiovasc Genet. 2013;6(4):337-46 (reported as p.R11240H, c.33719G>A)). This variant was previously reported in the SNPDatabase as rs764850788. Based on data from ExAC, the A allele has an overall frequency of less than 0.01% (3/103331). In the ESP, this variant was not observed in 6217 samples (12434 alleles) with coverage at this position. This amino acid position is highly conserved in available vertebrate species. In addition, this alteration is predicted to be tolerated by in silico analysis. Since supporting evidence is limited at this time, the clinical significance of this variant remains unclear. |
Revvity Omics, |
RCV000172341 | SCV003824921 | uncertain significance | not provided | 2019-06-06 | criteria provided, single submitter | clinical testing | |
New York Genome Center | RCV003227691 | SCV003925231 | uncertain significance | Dilated cardiomyopathy 1G; Hypertrophic cardiomyopathy 9 | 2022-07-06 | criteria provided, single submitter | clinical testing |