Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV002401700 | SCV002713338 | uncertain significance | Cardiovascular phenotype | 2018-11-26 | criteria provided, single submitter | clinical testing | The p.P5882Q variant (also known as c.17645C>A), located in coding exon 70 of the TTN gene, results from a C to A substitution at nucleotide position 17645. The proline at codon 5882 is replaced by glutamine, an amino acid with similar properties. This amino acid position is highly conserved in available vertebrate species. In addition, the in silico prediction for this alteration is inconclusive. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |