Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV001638403 | SCV001850012 | benign | not provided | 2015-07-22 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV002072944 | SCV002433765 | likely benign | Dilated cardiomyopathy 1G; Autosomal recessive limb-girdle muscular dystrophy type 2J | 2025-02-02 | criteria provided, single submitter | clinical testing | |
Women's Health and Genetics/Laboratory Corporation of America, |
RCV003317518 | SCV004020352 | likely benign | not specified | 2023-06-12 | criteria provided, single submitter | clinical testing | Variant summary: TTN c.49259-19_49259-18delinsTC alters a nucleotide located in the intronic region. SpliceAI predicts no significant impact on normal splicing. However, these predictions have yet to be confirmed by functional studies. The variant was absent in 270094 control chromosomes. The available data on variant occurrences in the general population are insufficient to allow any conclusion about variant significance. To our knowledge, no occurrence of c.49259-19_49259-18delinsTC in individuals affected with Dilated Cardiomyopathy and no experimental evidence demonstrating its impact on protein function have been reported. Two clinical diagnostic laboratories have submitted clinical-significance assessments for this variant to ClinVar after 2014 without evidence for independent evaluation. All laboratories classified the variant as benign/likely benign. Based on the evidence outlined above, the variant was classified as likely benign. |