Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
CHEO Genetics Diagnostic Laboratory, |
RCV001799213 | SCV002042577 | uncertain significance | Cardiomyopathy | 2019-12-24 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV002458612 | SCV002612653 | uncertain significance | Cardiovascular phenotype | 2020-09-01 | criteria provided, single submitter | clinical testing | The p.V11342A variant (also known as c.34025T>C), located in coding exon 131 of the TTN gene, results from a T to C substitution at nucleotide position 34025. The valine at codon 11342 is replaced by alanine, an amino acid with similar properties. This amino acid position is not well conserved in available vertebrate species. In addition, this alteration is predicted to be tolerated by in silico analysis. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |
Gene |
RCV005057622 | SCV005689816 | uncertain significance | not provided | 2024-08-09 | criteria provided, single submitter | clinical testing | Not observed at significant frequency in large population cohorts (gnomAD); Missense variant in a gene in which most reported pathogenic variants are truncating/loss of function; Has not been previously published as pathogenic or benign to our knowledge |