Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Genetics and Personalized Medicine Clinic, |
RCV003484462 | SCV004228502 | likely pathogenic | Autosomal recessive limb-girdle muscular dystrophy type 2J | criteria provided, single submitter | clinical testing | We found in compound heterozygous state in trans with FINMaj variant NM_001267550.2(TTN):c.107780_107790delinsTGAAAGAAAAA in two patients with Titin-related limb-girdle muscular dystrophy R10. |