Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Petrovsky National Research Centre of Surgery, |
RCV005055469 | SCV005689545 | likely pathogenic | Dilated cardiomyopathy 1G | 2024-10-21 | criteria provided, single submitter | clinical testing | The c.69261G>A (p.Trp23087*) nonsense variant in the TTN gene was found on WES data in a 60-y.o. female proband diagnosed with arrhythmogenic cardiomyopathy. This variant is absent in databases (gnomAD, LOVD) and predicted to introduce a premature translation termination codon. According to NMD Esc Predictor and AutoPVS1, mRNA carrying this variant, will be processed through nonsense-mediated decay mechanism, leading to haploinsufficiency. For these reasons, this variant has been classified as Likely Pathogenic. |