Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Laboratory for Molecular Medicine, |
RCV000152219 | SCV000200997 | uncertain significance | not specified | 2014-11-17 | criteria provided, single submitter | clinical testing | The p.Arg21896Trp variant in TTN has not been previously reported in individuals with cardiomyopathy, but has been identified in 1/3828 of African American chro mosomes by the NHLBI Exome Sequencing Project (http://evs.gs.washington.edu/EVS/ ; dbSNP rs369098292). Computational prediction tools and conservation analysis s uggest that this variant may impact the protein, though this information is not predictive enough to determine pathogenicity. In summary, the clinical significa nce of the p.Arg21896Trp variant is uncertain. |
Ambry Genetics | RCV002336304 | SCV002636590 | uncertain significance | Cardiovascular phenotype | 2020-03-17 | criteria provided, single submitter | clinical testing | The p.R15399W variant (also known as c.46195C>T), located in coding exon 153 of the TTN gene, results from a C to T substitution at nucleotide position 46195. The arginine at codon 15399 is replaced by tryptophan, an amino acid with dissimilar properties. This amino acid position is highly conserved in available vertebrate species. In addition, this alteration is predicted to be tolerated by in silico analysis. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |