Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV002368944 | SCV002659529 | uncertain significance | Cardiovascular phenotype | 2018-05-02 | criteria provided, single submitter | clinical testing | The p.V21154G variant (also known as c.63461T>G), located in coding exon 162 of the TTN gene, results from a T to G substitution at nucleotide position 63461. The valine at codon 21154 is replaced by glycine, an amino acid with dissimilar properties. This amino acid position is poorly conserved in available vertebrate species. In addition, the in silico prediction for this alteration is inconclusive. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |