Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV000246207 | SCV000318191 | uncertain significance | Cardiovascular phenotype | 2019-04-16 | criteria provided, single submitter | clinical testing | The p.D29958E variant (also known as c.89874C>G), located in coding exon 298 of the TTN gene, results from a C to G substitution at nucleotide position 89874. The aspartic acid at codon 29958 is replaced by glutamic acid, an amino acid with highly similar properties. This amino acid position is well conserved in available vertebrate species. In addition, this alteration is predicted to be possibly damaging and unknown by PolyPhen and SIFT in silico analyses, respectively. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |
CHEO Genetics Diagnostic Laboratory, |
RCV001170751 | SCV001333356 | uncertain significance | Cardiomyopathy | 2017-11-30 | criteria provided, single submitter | clinical testing |