Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Eurofins Ntd Llc |
RCV000591641 | SCV000706812 | uncertain significance | not provided | 2018-06-15 | criteria provided, single submitter | clinical testing | |
Women's Health and Genetics/Laboratory Corporation of America, |
RCV001193165 | SCV001361843 | uncertain significance | not specified | 2019-11-25 | criteria provided, single submitter | clinical testing | Variant summary: TTN c.91832T>C (p.Val30611Ala) results in a non-conservative amino acid change located in the A-band of the encoded protein sequence. Three of five in-silico tools predict a benign effect of the variant on protein function. The variant allele was found at a frequency of 6.4e-05 in 248956 control chromosomes (gnomAD). This frequency is not significantly higher than expected for a pathogenic variant in TTN causing Cardiomyopathy (6.4e-05 vs 0.00063), allowing no conclusion about variant significance. c.91832T>C has been reported in the literature in an individual affected with arrhythmogenic right ventricular cardiomyopathy/dysplasia (ARVC/D). The patient also carried two DSG2 variants, c.217-1G>T and p.F531C. Authors suggest that the F531C variant is the main reason for the ARVC/D with more severe phenotypes being presented due to the co-occurrence with the DSG2 splice variant (Lin_2018). A ClinVar submission (evaluation after 2014) cites the variant as uncertain significance. Based on the evidence outlined above, the variant was classified as uncertain significance. |
Gene |
RCV000591641 | SCV002102708 | likely benign | not provided | 2021-05-06 | criteria provided, single submitter | clinical testing |