Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Mayo Clinic Laboratories, |
RCV000660496 | SCV000782595 | uncertain significance | Primary ciliary dyskinesia 7 | 2017-03-03 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV001036806 | SCV001200189 | benign | Primary ciliary dyskinesia | 2024-02-16 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV001036806 | SCV004056449 | uncertain significance | Primary ciliary dyskinesia | 2023-07-13 | criteria provided, single submitter | clinical testing | The p.G4190D variant (also known as c.12569G>A), located in coding exon 77 of the DNAH11 gene, results from a G to A substitution at nucleotide position 12569. The glycine at codon 4190 is replaced by aspartic acid, an amino acid with similar properties. This amino acid position is conserved. In addition, this alteration is predicted to be tolerated by in silico analysis. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |