Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Diagnostics Services |
RCV001799549 | SCV002043758 | uncertain significance | Spinocerebellar ataxia 44 | 2021-10-14 | criteria provided, single submitter | clinical testing | The c.3405C>G variant is not present in publicly available population databases like 1000 Genomes, Exome Variant Server (EVS) and Exome Aggregation Consortium (ExAC). The heterozygous state of the variant is present in Genome Aggregation Database (gnomAD) and dbSNP at a very low frequency. The variant is not present in Indian Exome Database and in our in-house exome database. The variant was not earlier reported to ClinVar, Human Genome Mutation Database (HGMD) or OMIM databases in any affected individuals. Predictions from different in-silico pathogenicity prediction programs like SIFT, Polyphen-2, MutationTaster2, CADD etc. are contradictory but these predictions have not been confirmed by published functional studies. Due to lack of enough evidence the variant has been classified as uncertain significance. |