Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Institute of Human Genetics, |
RCV002250440 | SCV002520685 | pathogenic | Late-onset retinal degeneration | 2022-05-27 | criteria provided, single submitter | clinical testing | The variant c.562C>A (p.(Pro188Thr)) in exon 15 of the C1QTNF5-gene is not found in the gnomAD database, it affects a moderately conserved nucleotide, a highly conserved amino acid within a protein domain and there is a small physicochemical difference between Pro and Thr. This mutation has already been described to be pathogenic in the literature (PMID: 33949280) and functional studies have shown a deleterious effect of this variant on protein function (PMID: 28939808). Also, p.Pro188Thr is a missense mutation at an amino acid residue where another missense change determined to be pathogenic has been already described (p.Pro188Leu, PMID: 32036094). This variant has a pathogenic computational verdict based in silico prediction models. ACMG criteria used for classification: PS3, PM2, PM5, PP2, PP3, PP5. |
Institute of Human Genetics, |
RCV004816986 | SCV005072534 | likely pathogenic | Retinal dystrophy | 2022-01-01 | criteria provided, single submitter | clinical testing |