Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Laboratorio de Genetica e Diagnostico Molecular, |
RCV002253187 | SCV002523443 | likely benign | See cases | 2020-01-03 | criteria provided, single submitter | clinical testing | ACMG classification criteria: PM2, BP1, BP4 |
Labcorp Genetics |
RCV003094135 | SCV003472619 | uncertain significance | not provided | 2024-07-11 | criteria provided, single submitter | clinical testing | This sequence change replaces glutamic acid, which is acidic and polar, with lysine, which is basic and polar, at codon 990 of the ADNP protein (p.Glu990Lys). This variant is present in population databases (rs531230573, gnomAD 0.04%). This missense change has been observed in individual(s) with autism spectrum disorder (PMID: 30564305). ClinVar contains an entry for this variant (Variation ID: 1690769). An algorithm developed to predict the effect of missense changes on protein structure and function (PolyPhen-2) suggests that this variant is likely to be tolerated. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |
Fulgent Genetics, |
RCV005032200 | SCV005661460 | uncertain significance | ADNP-related multiple congenital anomalies - intellectual disability - autism spectrum disorder | 2024-06-12 | criteria provided, single submitter | clinical testing |