Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Center for Genomics, |
RCV000768302 | SCV000898937 | uncertain significance | Dyskeratosis congenita, autosomal recessive 5; Pulmonary fibrosis and/or bone marrow failure, Telomere-related, 3 | 2021-03-30 | criteria provided, single submitter | clinical testing | RTEL1 NM_032957.4 exon 3 p.Ser88Phe (c.263C>T): This variant has not been reported in the literature but is present in 1/30778 South Asian alleles in the Genome Aggregation Database (http://gnomad.broadinstitute.org/variant/20-62292811-C-T). Evolutionary conservation and computational predictive tools for this variant are unclear. In summary, data on this variant is insufficient for disease classification. Therefore, the clinical significance of this variant is uncertain. |