Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Johns Hopkins Genomics, |
RCV002282771 | SCV002570312 | uncertain significance | Pulmonary fibrosis and/or bone marrow failure, Telomere-related, 3 | 2022-01-11 | criteria provided, single submitter | clinical testing | This RTEL1 variant is absent from a large population dataset and has not been reported in ClinVar nor the literature, to our knowledge. Three bioinformatic tools queried predict that this substitution would be damaging and the histidine residue at this position is evolutionarily conserved across many of the species assessed. We consider the clinical significance of RTEL1 c.2944C>T to be uncertain at this time. |