Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Clinical Genomics Laboratory, |
RCV005052229 | SCV005685291 | uncertain significance | Hennekam lymphangiectasia-lymphedema syndrome 2 | 2024-06-20 | criteria provided, single submitter | clinical testing | A FAT4 c.8921A>G (p.Asn2974Ser) variant was identified at a near heterozygous allele fraction, which may be consistent with germline origin. This variant, to our knowledge, has not been reported in the medical literature and is observed on 16/1,613,892 alleles in the general population (gnomAD v4.1.0). Computational predictors suggest that this variant does not impact FAT4 function. Due to limited information, and based on ACMG/AMP guidelines for variant interpretation (Richards S et al., PMID: 25741868), the clinical significance of the FAT4 c.8921A>G (p.Asn2974Ser) variant is uncertain at this time. |