Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Clinical Genomics Laboratory, |
RCV004560384 | SCV005047080 | uncertain significance | Hennekam lymphangiectasia-lymphedema syndrome 2 | 2024-01-19 | criteria provided, single submitter | clinical testing | The FAT4 c.9203A>G (p.Asn3068Ser) variant was identified at a near heterozygous allele fraction of 41%, a frequency which may be consistent with it being of germline origin. Computational predictors suggest that this variant does not impact FAT4 function. This variant is only observed on 26/1,613,698 alleles in the general population (gnomAD v4.0.0), indicating it is not a common variant. This variant, to our knowledge, has not been reported in the medical literature. Due to conflicting information, and based on ACMG/AMP guidelines for variant interpretation (Richards S et al., PMID: 25741868), the clinical significance of the FAT4 c.9203A>G (p.Asn3068Ser) variant is uncertain at this time. |