Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Center for Human Genetics, |
RCV000211110 | SCV000268069 | likely pathogenic | Nance-Horan syndrome | 2015-01-01 | criteria provided, single submitter | literature only | |
Prevention |
RCV004730908 | SCV005338525 | pathogenic | NHS-related disorder | 2024-05-30 | no assertion criteria provided | clinical testing | The NHS c.694C>T variant is predicted to result in premature protein termination (p.Gln232*). This variant, previously reported as p.Q55X, has been documented in patients with Nance-Horan syndrome, including a female patient (Patient 5 in Fieremans et al 2016. PubMed ID: 27159028; Additional file 4 in Ling et al. 2019. PubMed ID: 30642278). This variant has not been reported in a large population database, indicating this variant is rare. Nonsense variants in NHS are expected to be pathogenic. This variant is interpreted as pathogenic. |