Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Revvity Omics, |
RCV001782554 | SCV002020198 | likely pathogenic | Autosomal recessive nonsyndromic hearing loss 18B | 2020-09-18 | criteria provided, single submitter | clinical testing | |
3billion | RCV001782554 | SCV002058262 | likely pathogenic | Autosomal recessive nonsyndromic hearing loss 18B | 2022-01-03 | criteria provided, single submitter | clinical testing | Canonical splice site: predicted to alter splicing and result in a loss or disruption of normal protein function through protein truncation. Multiple pathogenic variants are reported in the predicted truncated region (PVS1_VS). It is observed at an extremely low frequency in the gnomAD v2.1.1 dataset (total allele frequency: 0.000236, PM2_M). Therefore, this variant is classified as likely pathogenic according to the recommendation of ACMG/AMP guideline. |